Fever-induced epileptic encephalopathy in children (FIRES)
نویسندگان
چکیده
منابع مشابه
Elevated VGKC-complex antibodies in a boy with fever-induced refractory epileptic encephalopathy in school-age children (FIRES).
Fever-induced refractory epileptic encephalopathy in school-age children (FIRES) is a clinically recognized epileptic encephalopathy of unknown aetiology. Presentation in previously healthy children is characterized by febrile status epilepticus. A pharmacoresistant epilepsy ensues, occurring in parallel with dramatic cognitive decline and behavioural difficulties. We describe a case of FIRES i...
متن کامل18F-FDG PET reveals frontotemporal dysfunction in children with fever-induced refractory epileptic encephalopathy.
UNLABELLED Fever-induced refractory epileptic encephalopathy in school-age children (FIRES) is a recently described epileptic entity whose etiology remains unknown. Brain abnormalities shown by MRI are usually limited to mesial-temporal structures and do not account for the catastrophic neuropsychologic findings. METHODS We conducted FIRES studies in 8 patients, aged 6-13 y, using 18F-FDG PET...
متن کاملEpileptic Encephalopathy
Epileptic encephalopathies are conditions in which epileptic activity itself is postulated to contribute to severe cognitive and behavioural impairments above and beyond what might be expected from the underlying pathology alone. The term has been used in two ways: (1) as a generic classification term for epilepsies with severe cognitive and be-havioural outcomes and (2) as a pathophysiological...
متن کاملEpileptic Encephalopathy in Children with Risk Factors for Brain Damage
In the study of 887 new born infants with prenatal and perinatal risk factors for brain damage, 11 children with West syndrome that progressed into Lennox-Gastaut syndrome and another 4 children with Lennox-Gastaut syndrome that had not been preceded by West syndrome were found. In this study we present the main findings of these 15 subjects. In all infants multifactor antecedents were detected...
متن کاملExtremely sustained startle-induced clonus: Non epileptic motor attacks mimicking clonic seizures in children with encephalopathy
Clonus is a pathological motor pattern characterised by involuntary, rhythmic and brisk muscular contractions in response to peripheral stimuli producing muscle stretching. It indicates pathological involvement of the corticospinal tract and can be considered as a functional spastic movement disorder of variable clinical presentation and duration. We documented severe and prolonged episodes of ...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: HERALD of North-Western State Medical University named after I.I. Mechnikov
سال: 2019
ISSN: 2618-9704,2618-7116
DOI: 10.17816/mechnikov201810465-72